What are the complications associated with choledochal cyst?
Adults with choledochal cysts can present with one or more severe complications – eg, liver abscesses, cirrhosis, portal hypertension, recurrent pancreatitis, gallstones, cholangiocarcinoma. About 1-12% of patients present with spontaneous rupture and symptoms and signs of abdominal pain, sepsis and peritonitis.
What are the different types of choledochal cyst?
Types and locations of choledochal cysts Type 1 — a cyst of the extrahepatic bile duct, accounting for up to 90% of all choledochal cysts. Type 2 — an abnormal pouch or sac opening from the duct. Type 3 — a cyst inside the wall of the duodenum. Type 4 — cysts on both the intrahepatic and extrahepatic bile ducts.
What is a Type 2 choledochal cyst?
Types and locations of choledochal cysts Type 2 — an abnormal pouch or sac opening from the duct. Type 3 — a cyst inside the wall of the duodenum. Type 4 — cysts on both the intrahepatic and extrahepatic bile ducts.
What is the prevalence of choledochal cysts?
Introduction Choledochal cysts are rare cystic transformations of the biliary tree that are increasingly diagnosed in adult patients 1,2,3,4. These congenital lesions have a female:-male preponderance of 4:1, with an incidence in the West of between 1 in 50 000 and 1 in 200 000 live births 3; they are much more frequent in Asia 5,6.
What are the symptoms of choledochal cysts in adults?
We present the management of a series of adult patients with choledochal cysts and symptoms related to the presence of the cyst in situ. Their presentations did not follow any classical patterns. Many had episodic and non-specific symptoms, but all experienced abdominal pain and most had episodes of cholangitis.
What is the surgical strategy for choledochal cysts?
Choledochal cyst is rare in adults. The typical triad of abdominal pain, jaundice, and mass is uncommon in adults. The surgical strategy aims for single stage complete excision of the cyst with hepaticojejunostomy. 1. Introduction
What are the possible complications of choledochal cyst excision?
However, there is evidence that patients who have undergone complete excision of choledochal cyst have an increased risk of developing carcinoma of the intrahepatic bile duct. Long-term close follow-up of these patients for early detection of malignancy is required.34
How is a choledochal cyst removed?
The treatment of choice for choledochal cysts is complete excision. Patients with type I, II, or IV cysts are recommended for surgical excision due to the risk of malignancy, if they are deemed good surgical candidates.
What are the symptoms of choledochal cyst?
Symptoms of Choledochal Cyst
- Yellow color to the eyes and skin (jaundice)
- Pain in the upper-right belly (upper-right-quadrant pain)
- Soft mass that can be felt in the upper-right belly.
- Pale or clay-colored stools (feces)
- Fever, if they have an infection (cholangitis)
What is RPC medicine?
Recurrent pyogenic cholangitis (RPC) is characterized by repeated infections of the biliary system with the formation of stones and strictures. The management aims are to treat acute cholangitis, clear the biliary ductal debris and calculi, and eliminate predisposing factors of bile stasis.
What does RPC mean in medical terms?
Specialty. General surgery. Recurrent pyogenic cholangitis (RPC), also known as Hong Kong disease, Oriental cholangitis, and Oriental infestational cholangitis, is a chronic infection characterized by recurrent bouts of bacterial cholangitis with primary hepatolithiasis.